Mitochondrial_central_dogma mtDNA_maintenance mtDNA_replication mtDNA_nucleoid mtDNA_repair mtDNA_modifications mtDNA_stability_and_decay mtRNA_metabolism Transcription mtRNA_granules Polycistronic_mtRNA_processing mt-tRNA_modifications mt-rRNA_modifications mt-mRNA_modifications mtRNA_stability_and_decay Translation Mitochondrial_ribosome Mitochondrial_ribosome_assembly Translation_factors mt-tRNA_synthetases fMet_processing Protein_import_sorting_and_homeostasis Protein_import_and_sorting TOM SAM MIA40 TIM22_carrier_pathway TIM23_presequence_pathway Import_motor OXA Preprotein_cleavage Protein_homeostasis Proteases Chaperones OXPHOS OXPHOS_subunits OXPHOS_assembly_factors Complex_I CI_subunits CI_assembly_factors Complex_II CII_subunits CII_assembly_factors Complex_III CIII_subunits CIII_assembly_factors Complex_IV CIV_subunits CIV_assembly_factors Complex_V CV_subunits CV_assembly_factors Respirasome_assembly Cytochrome_C Metabolism Carbohydrate_metabolism Gluconeogenesis Malate-aspartate_shuttle Glycerol_phosphate_shuttle Pyruvate_metabolism TCA_cycle TCA-associated Itaconate_metabolism Ketone_metabolism Propanoate_metabolism Lipid_metabolism Fatty_acid_oxidation Type_II_fatty_acid_synthesis Lipoate_insertion Cardiolipin_synthesis Cholesterol_bile_acid_steroid_synthesis Cholesterol-associated Phospholipid_metabolism Eicosanoid_metabolism Amino_acid_metabolism Branched-chain_amino_acid_metabolism Branched-chain_amino_acid_dehydrogenase_complex Lysine_metabolism Serine_metabolism Glycine_metabolism Glycine_cleavage_system Glutamate_metabolism Proline_metabolism Glyoxylate_metabolism GABA_metabolism Catechol_metabolism Kynurenine_metabolism Urea_cycle Nucleotide_metabolism Nucleotide_import Nucleotide_synthesis_and_processing Creatine_metabolism Metals_and_cofactors Carnitine_synthesis_and_transport Carnitine_shuttle Coenzyme_A_metabolism Coenzyme_Q_metabolism Copper_metabolism Iron_homeostasis Heme_synthesis_and_processing Fe-S_cluster_biosynthesis Molybdenum_cofactor_synthesis_and_proteins NAD_biosynthesis_and_metabolism Tetrahydrobiopterin_synthesis Fe-S-containing_proteins Heme-containing_proteins Vitamin_metabolism Choline_and_betaine_metabolism Biotin_utilizing_proteins Vitamin_A_metabolism Vitamin_B1_metabolism Vitamin_B2_metabolism Vitamin_B6_metabolism Vitamin_B12_metabolism Vitamin_C_metabolism Vitamin_D_metabolism Folate_and_1-C_metabolism Detoxification Xenobiotic_metabolism ROS_and_glutathione_metabolism Amidoxime_reducing_complex Selenoproteins Electron_carriers Cytochromes Q-linked_reactions_other Sulfur_metabolism Small_molecule_transport SLC25A_family ABC_transporters Sideroflexins Calcium_uniporter Signaling Calcium_homeostasis Calcium_cycle Mitochondrial_permeability_transition_pore EF_hand_proteins Immune_response cAMP-PKA_signaling Mitochondrial_dynamics_and_surveillance Fusion Fission Organelle_contact_sites Intramitochondrial_membrane_interactions Trafficking Mitophagy Autophagy Apoptosis Cristae_formation MICOS_complex Mitochondrial_central_dogma Mitochondrial_central_dogma.mtDNA_maintenance Mitochondrial_central_dogma.mtDNA_maintenance.mtDNA_replication Mitochondrial_central_dogma.mtDNA_maintenance.mtDNA_nucleoid Mitochondrial_central_dogma.mtDNA_maintenance.mtDNA_repair Mitochondrial_central_dogma.mtDNA_maintenance.mtDNA_modifications Mitochondrial_central_dogma.mtDNA_maintenance.mtDNA_stability_and_decay Mitochondrial_central_dogma.mtRNA_metabolism Mitochondrial_central_dogma.mtRNA_metabolism.Transcription Mitochondrial_central_dogma.mtRNA_metabolism.mtRNA_granules Mitochondrial_central_dogma.mtRNA_metabolism.Polycistronic_mtRNA_processing Mitochondrial_central_dogma.mtRNA_metabolism.mt-tRNA_modifications Mitochondrial_central_dogma.mtRNA_metabolism.mt-rRNA_modifications Mitochondrial_central_dogma.mtRNA_metabolism.mt-mRNA_modifications Mitochondrial_central_dogma.mtRNA_metabolism.mtRNA_stability_and_decay Mitochondrial_central_dogma.Translation Mitochondrial_central_dogma.Translation.Mitochondrial_ribosome Mitochondrial_central_dogma.Translation.Mitochondrial_ribosome_assembly Mitochondrial_central_dogma.Translation.Translation_factors Mitochondrial_central_dogma.Translation.mt-tRNA_synthetases Mitochondrial_central_dogma.Translation.fMet_processing Protein_import_sorting_and_homeostasis Protein_import_sorting_and_homeostasis.Protein_import_and_sorting Protein_import_sorting_and_homeostasis.Protein_import_and_sorting.TOM Protein_import_sorting_and_homeostasis.Protein_import_and_sorting.SAM Protein_import_sorting_and_homeostasis.Protein_import_and_sorting.MIA40 Protein_import_sorting_and_homeostasis.Protein_import_and_sorting.TIM22_carrier_pathway Protein_import_sorting_and_homeostasis.Protein_import_and_sorting.TIM23_presequence_pathway Protein_import_sorting_and_homeostasis.Protein_import_and_sorting.Import_motor Protein_import_sorting_and_homeostasis.Protein_import_and_sorting.OXA Protein_import_sorting_and_homeostasis.Protein_import_and_sorting.Preprotein_cleavage Protein_import_sorting_and_homeostasis.Protein_homeostasis Protein_import_sorting_and_homeostasis.Protein_homeostasis.Proteases Protein_import_sorting_and_homeostasis.Protein_homeostasis.Chaperones OXPHOS OXPHOS.OXPHOS_subunits OXPHOS.OXPHOS_assembly_factors OXPHOS.Complex_I OXPHOS.Complex_I.CI_subunits OXPHOS.Complex_I.CI_assembly_factors OXPHOS.Complex_II OXPHOS.Complex_II.CII_subunits OXPHOS.Complex_II.CII_assembly_factors OXPHOS.Complex_III OXPHOS.Complex_III.CIII_subunits OXPHOS.Complex_III.CIII_assembly_factors OXPHOS.Complex_IV OXPHOS.Complex_IV.CIV_subunits OXPHOS.Complex_IV.CIV_assembly_factors OXPHOS.Complex_V OXPHOS.Complex_V.CV_subunits OXPHOS.Complex_V.CV_assembly_factors OXPHOS.Respirasome_assembly OXPHOS.Cytochrome_C Metabolism Metabolism.Carbohydrate_metabolism Metabolism.Carbohydrate_metabolism.Gluconeogenesis Metabolism.Carbohydrate_metabolism.Malate-aspartate_shuttle Metabolism.Carbohydrate_metabolism.Glycerol_phosphate_shuttle Metabolism.Carbohydrate_metabolism.Pyruvate_metabolism Metabolism.Carbohydrate_metabolism.TCA_cycle Metabolism.Carbohydrate_metabolism.TCA-associated Metabolism.Carbohydrate_metabolism.Itaconate_metabolism Metabolism.Carbohydrate_metabolism.Ketone_metabolism Metabolism.Carbohydrate_metabolism.Propanoate_metabolism Metabolism.Lipid_metabolism Metabolism.Lipid_metabolism.Fatty_acid_oxidation Metabolism.Lipid_metabolism.Type_II_fatty_acid_synthesis Metabolism.Lipid_metabolism.Lipoate_insertion Metabolism.Lipid_metabolism.Cardiolipin_synthesis Metabolism.Lipid_metabolism.Cholesterol_bile_acid_steroid_synthesis Metabolism.Lipid_metabolism.Cholesterol-associated Metabolism.Lipid_metabolism.Phospholipid_metabolism Metabolism.Lipid_metabolism.Eicosanoid_metabolism Metabolism.Amino_acid_metabolism Metabolism.Amino_acid_metabolism.Branched-chain_amino_acid_metabolism Metabolism.Amino_acid_metabolism.Branched-chain_amino_acid_dehydrogenase_complex Metabolism.Amino_acid_metabolism.Lysine_metabolism Metabolism.Amino_acid_metabolism.Serine_metabolism Metabolism.Amino_acid_metabolism.Glycine_metabolism Metabolism.Amino_acid_metabolism.Glycine_cleavage_system Metabolism.Amino_acid_metabolism.Glutamate_metabolism Metabolism.Amino_acid_metabolism.Proline_metabolism Metabolism.Amino_acid_metabolism.Glyoxylate_metabolism Metabolism.Amino_acid_metabolism.GABA_metabolism Metabolism.Amino_acid_metabolism.Catechol_metabolism Metabolism.Amino_acid_metabolism.Kynurenine_metabolism Metabolism.Amino_acid_metabolism.Urea_cycle Metabolism.Nucleotide_metabolism Metabolism.Nucleotide_metabolism.Nucleotide_import Metabolism.Nucleotide_metabolism.Nucleotide_synthesis_and_processing Metabolism.Nucleotide_metabolism.Creatine_metabolism Metabolism.Metals_and_cofactors Metabolism.Metals_and_cofactors.Carnitine_synthesis_and_transport Metabolism.Metals_and_cofactors.Carnitine_shuttle Metabolism.Metals_and_cofactors.Coenzyme_A_metabolism Metabolism.Metals_and_cofactors.Coenzyme_Q_metabolism Metabolism.Metals_and_cofactors.Copper_metabolism Metabolism.Metals_and_cofactors.Iron_homeostasis Metabolism.Metals_and_cofactors.Heme_synthesis_and_processing Metabolism.Metals_and_cofactors.Fe-S_cluster_biosynthesis Metabolism.Metals_and_cofactors.Molybdenum_cofactor_synthesis_and_proteins Metabolism.Metals_and_cofactors.NAD_biosynthesis_and_metabolism Metabolism.Metals_and_cofactors.Tetrahydrobiopterin_synthesis Metabolism.Metals_and_cofactors.Fe-S-containing_proteins Metabolism.Metals_and_cofactors.Heme-containing_proteins Metabolism.Vitamin_metabolism Metabolism.Vitamin_metabolism.Choline_and_betaine_metabolism Metabolism.Vitamin_metabolism.Biotin_utilizing_proteins Metabolism.Vitamin_metabolism.Vitamin_A_metabolism Metabolism.Vitamin_metabolism.Vitamin_B1_metabolism Metabolism.Vitamin_metabolism.Vitamin_B2_metabolism Metabolism.Vitamin_metabolism.Vitamin_B6_metabolism Metabolism.Vitamin_metabolism.Vitamin_B12_metabolism Metabolism.Vitamin_metabolism.Vitamin_C_metabolism Metabolism.Vitamin_metabolism.Vitamin_D_metabolism Metabolism.Vitamin_metabolism.Folate_and_1-C_metabolism Metabolism.Detoxification Metabolism.Detoxification.Xenobiotic_metabolism Metabolism.Detoxification.ROS_and_glutathione_metabolism Metabolism.Detoxification.Amidoxime_reducing_complex Metabolism.Detoxification.Selenoproteins Metabolism.Electron_carriers Metabolism.Electron_carriers.Cytochromes Metabolism.Electron_carriers.Q-linked_reactions_other Metabolism.Sulfur_metabolism Small_molecule_transport Small_molecule_transport.SLC25A_family Small_molecule_transport.ABC_transporters Small_molecule_transport.Sideroflexins Small_molecule_transport.Calcium_uniporter Signaling Signaling.Calcium_homeostasis Signaling.Calcium_homeostasis.Calcium_cycle Signaling.Calcium_homeostasis.Mitochondrial_permeability_transition_pore Signaling.Calcium_homeostasis.EF_hand_proteins Signaling.Immune_response Signaling.cAMP-PKA_signaling Mitochondrial_dynamics_and_surveillance Mitochondrial_dynamics_and_surveillance.Fusion Mitochondrial_dynamics_and_surveillance.Fission Mitochondrial_dynamics_and_surveillance.Organelle_contact_sites Mitochondrial_dynamics_and_surveillance.Intramitochondrial_membrane_interactions Mitochondrial_dynamics_and_surveillance.Trafficking Mitochondrial_dynamics_and_surveillance.Mitophagy Mitochondrial_dynamics_and_surveillance.Autophagy Mitochondrial_dynamics_and_surveillance.Apoptosis Mitochondrial_dynamics_and_surveillance.Cristae_formation Mitochondrial_dynamics_and_surveillance.Cristae_formation.MICOS_complex AARS2 APEX1 DNA2 ATAD3A APEX1 METTL4 ENDOG ALKBH1 MRPL12 ALKBH1 ELAC2 ALKBH1 METTL15 ANGEL2 ENDOG AARS2 AURKAIP1 DDX28 C12orf65 AARS2 METAP1D AFG1L AGK TOMM20 MTX1 AIFM1 AGK ROMO1 DNAJC15 OXA1L IMMP1L AFG1L AFG1L DNAJA3 ACAD9 ATP5F1A ACAD9 ACAD9 MT-ND1 ACAD9 SDHA SDHA SDHAF1 BCS1L CYC1 BCS1L CEP89 COX4I1 CEP89 ATP5F1A ATP5F1A ATPAF1 COX7A2L CYCS AADAT ABHD11 MDH2 GOT2 GPD2 DLAT ACO2 ABHD11 ACOD1 ACAA2 MCEE ACAA1 ACAA2 ACACA GCSH AGPAT4 CYP11A1 FDPS ACP6 MGST3 AADAT ACAD8 BCKDHA AADAT AGXT ALDH7A1 AMT GLS ALDH18A1 AGXT ABAT COMT GOT2 CA5A AK2 SLC25A23 AK2 CKMT1A ABAT CPT1A CPT1A COASY COQ10A CHCHD7 FAM210B ABCB10 ABCB7 ABCB7 KMO PCBD2 ABAT CYB5B ACACA ALDH7A1 ACACA AKR1B10 SLC25A19 FLAD1 PLPBP MMAA GLRX2 CYP24A1 ALDH1L1 ABHD10 ABHD10 AIFM2 CYB5B GPX1 CHDH CYB5B CHDH ETHE1 ABCA9 MTCH1 ABCA9 SFXN1 MCU ACOD1 EFHD1 LETM1 PPIF EFHD1 ACOD1 ADCY10 AHCYL1 ARL2 ARMC10 AHCYL1 ATAD3A ARMC10 BCL2L13 BCL2L13 AIFM1 APOO APOO ALKBH1 ATAD3A EXOG ATAD3B EXOG EXOG ANGEL2 MTERF1 DDX28 FASTK CDK5RAP1 METTL17 MTPAP FASTK AURKAIP1 CHCHD1 DHX30 COA3 CARS2 MTFMT AFG3L2 AIFM1 TOMM22 MTX2 CHCHD4 TIMM22 TIMM17A DNAJC19 IMMP2L AFG3L2 AFG3L2 DNLZ AIFM1 ATP5F1B AIFM1 AIFM1 MT-ND2 AIFM1 SDHAF1 SDHB SDHAF2 CYC1 MT-CYB LYRM7 CMC1 COX4I2 CMC1 ATP5F1B ATP5F1B ATPAF2 HIGD1A HCCS AASS ACAA2 MPC1 MDH2 DLD CS ACLY AUH ACAT1 MMUT ACAA2 ACACB ACSF3 LIAS AGPAT5 CYP11B1 IDI1 AGK PTGES2 AASS ACADSB BCKDHB AASS SDSL AMT DLD GLS2 ALDH4A1 AGXT2 ADHFE1 MAOA KMO CA5B AK3 SLC25A24 AK3 CKMT1B ABCB10 CPT1B CPT1B NUDT19 COQ10B COX11 FTH1 ABCB6 BOLA1 MOCS1 KYAT3 QDPR ACO2 CYC1 ACACB CHDH ACACB BCO2 RFK PNPO MMAB TXN2 CYP27B1 ALDH1L2 ACSM2A ACSM2A ALDH3A2 CYB5R3 GPX4 CYB5B CYC1 DHODH GOT2 ABCB10 MTCH2 ABCB10 SFXN2 MCUB ADCY10 LETM1 MCU SLC25A31 MICU1 C1QBP AKAP1 AIFM1 MFN1 DNM1L ATAD3A ATAD3B ARMCX1 FKBP8 FKBP8 AIFM2 APOOL APOOL ANGEL2 ATAD3B LIG3 MTERF1 LIG3 MGME1 CDK5RAP1 MTRES1 DHX30 FASTKD1 DUS2 METTL5 MYG1 FASTKD1 C12orf65 DAP3 ERAL1 COX14 DARS2 PDF AGK CHCHD4 TOMM34 SAMM50 GFER TIMM29 TIMM17B GRPEL1 MIPEP ATAD1 ATAD1 FKBP10 ATP5F1A ATP5F1C ATPAF1 COA1 MT-ND3 COA1 SDHAF2 SDHC SDHAF3 LYRM7 UQCR10 TTC19 CMC2 COX5A CMC2 ATP5F1C ATP5F1C ATPSCKMT HIGD2A ABAT ACAT1 MPC1L SLC25A10 MPC1 DLD D2HGDH CLYBL BDH1 PCCA ACACA ACAD10 CBR4 LIPT1 CRLS1 CYP11B2 AGPAT4 ZADH2 ABAT ACAT1 BCKDK ACAA2 SFXN1 CHDH GCSH GLUD1 OAT ALDH4A1 AKR7A2 MAOB KYAT3 CPS1 AK4 SLC25A25 AK4 CKMT2 ABCB6 CPT1C CPT1C NUDT8 COQ2 COX17 FTMT ABCB7 BOLA3 MTARC1 NADK2 SPR AIFM3 CYCS AKR1B10 DMGDH MCCC1 DHRS4 SLC25A32 MMADHC FDX1 ALDH7A1 ACSM5 ACSM5 ALDH7A1 MTARC1 SELENOO CYC1 CYCS ETFA MPST ABCB6 SLC25A1 ABCB6 SFXN3 MICU1 AKAP1 MCU MCUB SLC25A4 MICU2 IFI27 AKAP10 AIFM2 MFN2 FIS1 ATAD3B CHCHD3 ARMCX3 FUNDC1 FUNDC1 AIFM3 ATP5MD CHCHD3 APEX1 DNA2 MGME1 MTERF2 OGG1 DDX28 POLRMT ERAL1 FASTKD2 GTPBP3 MRM1 PDE12 FASTKD2 CARS2 GADD45GIP1 FASTKD2 GFM1 EARS2 AIFM1 DNAJC11 TOMM40 TIMM21 GRPEL2 PMPCA ATP23 ATP23 HSPD1 ATP5F1B ATP5F1D ATPAF2 DMAC1 MT-ND4 DMAC1 SDHAF3 SDHD SDHAF4 MT-CYB UQCR11 UQCC1 COA1 COX5B COA1 ATP5F1D ATP5F1D FMC1 RAB5IF ABCB10 ACLY MPC2 SLC25A11 MPC1L DLST FAHD1 SUCLA2 HADHB PCCB ACACB ACAD11 HSD17B8 LIPT2 GPAM CYP27A1 AGPAT5 ACAA2 ALDH6A1 DBT ACAT1 SFXN3 DLD GLDC GLUD2 PRODH GOT2 ALDH5A1 NAGS ANTKMT SLC25A31 CMPK2 GATM ABCB7 CPT2 CPT2 PANK2 COQ3 COX19 SLC25A28 ALAS1 CISD1 MTARC2 NAXD BOLA1 CYP11A1 ALDH1L1 ETFA PC RDH13 MMUT FDXR AMT AIFM2 AKR1B10 ALDH9A1 MTARC2 TXNRD1 CYCS MT-CYB ETFB MSRA ABCB7 SLC25A10 ABCB7 SFXN4 MICU2 AKAP10 MCUB MICU1 SLC25A5 MICU3 MAVS PDE2A AIFM3 MIGA1 MFF FKBP8 DNAJC11 MGARP MARCHF5 MARCHF5 BAD ATP5ME CHCHD6 ATAD3A ENDOG POLG POLDIP2 POLB DHX30 TEFM FASTK FASTKD3 HSD17B10 MRM2 FASTKD3 CHCHD1 MRPL1 GRSF1 GFM2 FARS2 ATAD1 DNAJC15 TOMM40L TIMM23 PAM16 PMPCB CASP3 CASP3 HSPE1 ATP5F1C ATP5F1E ATPSCKMT DMAC2 MT-ND4L DMAC2 SDHAF4 TTC19 UQCRB UQCC2 COA3 COX6A1 COA3 ATP5F1E ATP5F1E TMEM70 ABCB6 ACO2 PC SLC25A12 MPC2 FH L2HGDH SUCLG1 HMGCL ACAD10 ACADL HTD2 GPAT2 DHRS1 CHPT1 ACAD8 AUH DLD ALDH7A1 SHMT2 DMGDH GOT2 PYCR1 GRHPR ALDH9A1 OTC CKMT1A SLC25A33 DGUOK ACO2 SLC25A20 SLC25A20 SLC25A42 COQ4 SCO1 SLC25A37 ALAS2 CISD3 SUOX NAXE BOLA3 CYP11B1 ALDH1L2 ETFB PCCA RDH14 CHDH AKR1B10 AKR7A2 CAT TXNRD2 DHODH ETFBKMT MSRB2 ABCB8 SLC25A11 ABCB8 SFXN5 MICU3 BLOC1S1 MICU1 MICU2 SLC25A6 RHOT1 NLRX1 PRKACA APOO MIGA2 MIEF1 FUNDC2 MTX1 MYO19 NIPSNAP1 NBR1 BAK1 ATP5MG IMMT ATAD3B EXOG POLG2 POLG POLG DUS2 TFAM FASTKD1 FASTKD5 MTO1 MRM3 FASTKD5 COA3 MRPL10 GTPBP10 HEMK1 GARS1 ATP23 DNAJC19 TOMM5 TIMM50 TIMM44 UQCRC1 CASP8 CASP9 MAIP1 ATP5F1D ATP5IF1 BCS1L ECSIT MT-ND5 ECSIT SDHB UQCC1 UQCRC1 UQCC3 COA4 COX6A2 COA4 ATP5IF1 ATP5IF1 ABCB7 ACOD1 PCK2 SLC25A13 PDHA1 IDH2 ME2 SUCLG2 HMGCS2 ACAD11 ACADM MCAT HADHA FDX1 GPAM ACADSB BCAT2 PPM1K DHTKD1 ETFA GPT2 PYCR2 HOGA1 GLUD1 SLC25A13 CKMT1B SLC25A36 DHODH AIFM3 TMLHE COQ5 SCO2 COX10 FDX1 NMNAT3 CISD1 CYP11B2 ALDH7A1 ETFDH DMGDH AKR7A2 ALDH1B1 GLRX2 ETFA ETFDH SLC25A14 ABCD1 SLC25A12 ABCD1 SMDT1 C1QBP MICU2 MICU3 VDAC1 RHOT2 SPHKAP APOOL MTCH2 MIEF2 MFN1 MTX2 RHOT1 NIPSNAP2 NIPSNAP1 BAX CHCHD3 MICOS10 AURKAIP1 LIG3 POLRMT POLG2 PRIMPOL ELAC2 TFB2M FASTKD2 GRSF1 NSUN2 MTPAP GRSF1 COX14 MRPL11 MALSU1 MRPL58 GATB CASP3 GFER TOMM6 UQCRC2 CASP9 CLPB NRDC ATP5F1E ATP5MC1 CEP89 FOXRED1 MT-ND6 FOXRED1 SDHC UQCC2 UQCRC2 COA5 COX6B1 COA5 ATP5MC1 ATP5MC1 ABHD10 AUH SLC25A1 PDHA2 IDH3A ME3 OXCT1 ACADL ACADS MECR PGS1 FDXR GPAT2 ACAT1 BCKDHA DLD ETFB NAT8L LDHB GLUD2 SLC25A15 CKMT2 SLC25A4 DTYMK ALAS1 COQ6 SLC25A3 COX15 FDX2 NNT CISD3 CYP24A1 AMT SARDH FPGS ALDH1B1 ALDH2 GPX1 ETFB ETFRF1 SLC25A30 ABCD2 SLC25A13 ABCD2 CSKMT MICU3 SLC25A3 VDAC3 SLC25A12 ARL2 OMA1 MTFP1 MFN2 MTX3 RHOT2 PARK7 NIPSNAP2 BBC3 CHCHD6 MICOS13 C12orf65 METTL4 RNASEH1 POLRMT RECQL4 ENDOG TOP1MT FASTKD5 HSD17B10 NSUN3 MYG1 LACTB2 DAP3 MRPL12 METTL17 MRRF GATC CASP8 GRPEL1 TOMM7 XPNPEP3 CLPB CLPP PHB ATP5IF1 ATP5MC2 CMC1 LYRM2 NDUFA1 LYRM2 SDHD UQCC3 UQCRFS1 COA6 COX6B2 COA6 ATP5MC2 ATP5MC2 ABHD11 BDH1 SLC25A10 PDHB IDH3B MPC1 OXCT2 ACADM ACADSB NDUFAB1 PLD6 HINT2 LACTB ADHFE1 BCKDHB DLST ETFDH SLC25A12 PRODH2 CMPK2 SLC25A41 DUT ALAS2 COQ7 CPOX FDXR NOCT DNA2 CYP27A1 BCO2 GTPBP3 ALDH2 BPHL GPX4 ETFBKMT GPD2 SQOR ABCD3 SLC25A14 ABCD3 DELE1 PPIF SLC8B1 SLC25A13 ARMC10 OPA1 MTFR1 MIGA2 SAMM50 PARL PARK7 BCL2 IMMT CARS2 MGME1 SSBP1 SSBP1 UNG ERAL1 GRSF1 PRORP OSGEPL1 NGRN LRPPRC DARS2 MRPL13 MIEF1 MTIF2 HARS2 CASP9 GRPEL2 TOMM70 CLPP CLPX PHB2 ATP5MC1 ATP5MC3 CMC2 MT-ND1 NDUFA10 NDUFAF1 UQCR10 UQCRH COA7 COX6C COA7 ATP5MC3 ATP5MC3 ACAA1 CLYBL SLC25A11 PDHX IDH3G MPC1L ACADS ACADVL OXSM PLSCR3 HSD17B10 OSBPL1A AGMAT BCKDK ECHS1 GCAT DGUOK SLC25A5 FHIT BOLA1 COQ8A FABP1 FXN NUDT13 ETFDH CYP27B1 CHDH MTFMT ALDH3A2 CBR3 GSR ETFDH PRODH SUOX CCDC51 SLC25A15 EFHD1 RHOT1 SMDT1 SLC25A23 ARMCX1 PLD6 MTFR2 PIGBOS1 SLC25A46 PGAM5 PARL BCL2A1 MICOS10 CDK5RAP1 MTERF1 TFAM TFAM FASTK HSD17B10 PTCD2 PUS1 NSUN4 MTPAP DDX28 MRPL14 MPV17L2 MTIF3 IARS2 CHCHD4 IMMP1L CLPX HTRA2 TIMM10 ATP5MC2 ATP5MD COA1 MT-ND2 NDUFA11 NDUFAF2 UQCR11 UQCRQ COA8 COX7A1 COA8 ATP5MD ATP5MD ACAA2 CS PDK1 MDH2 MPC2 ACADSB ACAT1 PNPLA8 HSD17B8 PGS1 AGXT DBT ETFA GCSH DHODH SLC25A6 GUK1 BOLA3 COQ8B FDX1 GLRX5 SIRT3 FDX1 MT-CO1 CYP24A1 MTHFD1L ALDH7A1 CYB5B HAGH ETFRF1 PRODH2 TST LETMD1 SLC25A16 FUNDC2 RHOT2 SLC25A24 ARMCX3 MUL1 RMDN3 PINK1 PGAM5 BCL2L1 MICOS13 CHCHD1 MTERF2 TFB2M TWNK FASTKD1 MRM1 TBRG4 QTRT1 RCC1L PDE12 DHX30 MRPL15 MRM2 MTRF1 KARS1 CLPB IMMP2L DNAJA3 IDE TIMM10B ATP5MC3 ATP5ME COA3 MT-ND3 NDUFA12 NDUFAF3 UQCRB COX10 COX7A2 COX10 ATP5ME ATP5ME ACACA D2HGDH PDK2 MRPS36 PC ACADVL ACOT11 PRELID1 OSBPL1A PISD AGXT2 DLD ETFB GLDC DTYMK HINT1 CHCHD7 COQ9 FDX2 GRPEL1 SIRT4 FDX2 MT-CYB CYP27B1 MTHFD2 ALDH9A1 CYB5R3 MGST1 GPD2 SQOR TSTD1 MCU SLC25A18 IFI27 SLC25A12 SLC25A25 ATAD3A OMA1 SPIRE1 PRKN PINK1 BCL2L10 OPA1 COA3 MUTYH TOP1MT FASTKD2 MRM2 TRMT10C RPUSD4 RPUSD3 PNPT1 EARS2 MRPL16 MRM3 MTRF1L LARS2 CLPP MIPEP DNAJC4 IMMP1L TIMM13 ATP5MD ATP5MF COA4 MT-ND4 NDUFA13 NDUFAF4 UQCRC1 COX11 COX7A2L COX11 ATP5MF ATP5MF ACACB DCXR PDK3 OGDH PCK2 ACAT1 ACSF2 PRELID3A SCP2 PNPLA8 AKR7A2 ECHS1 ETFDH GLYAT DUT NME3 CISD1 PDSS1 FDXR GRPEL2 SIRT5 FECH SDHC DHRS4 MTHFD2L BPHL DHRS2 MSRA MT-CYB MCUB SLC25A19 LETM1 SLC25A13 ATAD3B RAB24 STX17 TOMM7 PRKN BCL2L11 COX14 OGG1 TOP3A FASTKD3 MRPL47 YBEY THG1L RPUSD4 REXO2 ERAL1 MRPL17 MTERF3 TACO1 MARS2 CLPX MTX1 DNLZ IMMP2L TIMM8A ATP5ME ATP5MG COA5 MT-ND4L NDUFA2 NDUFAF5 UQCRC2 COX14 COX7B COX14 ATP5MG ATP5MG ACAD10 DLAT PDK4 OGDHL SFXN5 ACOT11 ACSL1 PTPMT1 STAR PRDX6 ALDH18A1 ETFA GCDH SARDH FHIT NME4 CISD3 PDSS2 FECH HSCB SLC25A51 GLRX2 SDHD DMGDH MTHFS CAT EPHX2 MSRB2 PRODH MICU1 SLC25A20 LYPLA1 SLC25A23 ATP5MD SLC25A46 SYNJ2BP USP30 RAB24 BCL2L13 DAP3 PIF1 TWNK FASTKD5 MRPS7 TRIT1 TFB1M RNASEH1 EXD2 MRPL18 MTERF4 TIMM21 NARS2 DNAJA3 MTX2 FKBP10 LACTB TIMM8B ATP5MF ATP5MPL COA6 MT-ND5 NDUFA3 NDUFAF6 UQCRFS1 COX15 COX7B2 COX15 ATP5MPL ATP5MPL ACAD11 DLD PDP1 SDHA SLC25A1 ACOT13 ACSL6 TAMM41 TSPO PRELID1 ALDH4A1 ETFB HADH SHMT2 GATM NME6 COASY HCCS HSPA9 SLC25A52 GLRX5 ETFA MTO1 CBR3 GLYAT MSRB3 PRODH2 MICU2 SLC25A21 MACROD1 SLC25A24 ATP5ME SPIRE1 VDAC1 VPS13D SNAP29 BCL2L2 DARS2 POLB GRSF1 MRPS9 TRMT1 TRIT1 SLIRP FARS2 MRPL19 MTG1 TSFM PARS2 DNAJC11 NRDC HSPD1 LAP3 TIMM9 ATP5MG ATP5PB COA7 MT-ND6 NDUFA5 NDUFAF7 UQCRH COX16 COX7C COX16 ATP5PB ATP5PB ACAD8 DLST PDP2 SDHB SLC25A11 ACOT2 ACSM1 TAZ PRELID3A ALDH5A1 ETFDH HADHB SLC25A38 GUK1 NT5DC2 COQ10A PPOX IBA57 ISCA1 ETFB QDPR CYB5B GSTK1 NIT1 SQOR MICU3 SLC25A22 MAVS SLC25A25 ATP5MG STX17 STX17 BID DDX28 POLDIP2 GTPBP3 MTPAP TRMT10C TRMT2B SUPV3L1 FASTKD2 MRPL2 MTG2 TUFM QRSL1 DNAJC15 OXA1L HSPE1 LONP1 TRAP1 ATP5MPL ATP5PD COA8 NDUFA1 NDUFA6 NDUFAF8 UQCRQ COX17 COX8A COX17 ATP5PD ATP5PD ACADL FAHD1 PDPR SDHC ACOT7 ACSM2A TRIAP1 PRELID3B ALDH6A1 HADHA SLC25A29 HINT1 NT5M COQ10B SLC25A38 ISCA1 ISCA2 ETFDH SARDH CYB5R3 GSTZ1 OXR1 MPC1 SLC25A23 MCRIP2 SLC25A3 BAD TOMM7 BIK DHX30 POLG HSD17B10 NOA1 TRMT2B TRMT61B TBRG4 GADD45GIP1 MRPL20 NGRN RARS2 DNAJC19 PAM16 HTRA2 METAP1D ATP5PB ATP5PF COX10 NDUFA10 NDUFA7 NUBPL COX18 COX8C COX18 ATP5PF ATP5PF ACADM FH SDHD ACOT9 ACSM2B PTPMT1 ALDH7A1 HIBADH NME3 NUDT2 COQ2 ISCA2 ISCU FDX1 SFXN1 DHRS2 MAOA PRDX2 MPC1L SLC25A24 MCU SLC25A31 BAK1 USP30 BNIP3 DNA2 POLG2 LACTB2 PRORP TRMT5 TRUB2 GARS1 MRPL21 NOA1 SARS2 DNAJC4 PMPCA IDE MIPEP ATP5PD ATP5PO COX11 NDUFA11 NDUFA8 TIMMDC1 COX19 MT-CO1 COX19 ATP5PO ATP5PO ACADS GLYCTK SUCLA2 ACP6 ACSM3 SERAC1 ALDH9A1 HIBCH NME4 NUDT5 COQ3 ISCU LIAS FDXR SFXN3 EPHX2 MAOB PRDX3 MPC2 SLC25A25 MCUB SLC25A4 BAX VPS13D BNIP3L DUS2 POLQ LRPPRC PTCD1 TRMT61B GATB MRPL22 NSUN4 TARS2 DNLZ PMPCB IMMP1L NLN ATP5PF COX4I1 COX14 NDUFA12 NDUFA9 TMEM126A COX20 MT-CO2 COX20 ATPAF1 DMAC2L ACADSB GOT2 SUCLG1 ACSF2 ACSM4 SPHK2 AMT HMGCL NME6 NUDT9 COQ4 LYRM4 NDUFS1 FLAD1 SHMT2 GLRX2 MGST1 PRDX4 MPV17 SLC25A26 MICU1 SLC25A5 BBC3 BOK EARS2 POLRMT METTL15 PTCD2 TRMU GATC MRPL23 PTCD3 VARS2 FKBP10 ROMO1 IMMP2L OMA1 ATP5PO COX4I2 COX15 NDUFA13 NDUFAB1 TMEM126B COX4I1 MT-CO3 HIGD1A ATPAF2 MT-ATP6 ACADVL GPD2 SUCLG2 ACSF3 ACSM5 SPTLC2 ARG2 HSD17B10 NT5DC2 PAICS COQ5 NDUFAB1 NDUFS2 FPGS SLC25A32 GLYAT MPST PRDX5 MPV17L SLC25A27 MICU2 SLC25A6 BCL2 CASP3 ELAC2 PPA2 METTL17 PUS1 TRNT1 GFM1 MRPL24 RBFA WARS2 GFER SAMM50 LACTB PARL ATPAF1 COX5A COX16 NDUFA2 NDUFB1 TMEM186 COX4I2 NDUFA4 PET100 ATPSCKMT MT-ATP8 ACAT1 HADHB ACSL1 ACSS1 STARD7 AUH IVD NT5M SUCLA2 COQ6 NFS1 NDUFS7 GLRX2 SLC25A38 GPX1 MTARC1 PRDX6 MRS2 SLC25A28 MICU3 SLC8B1 BCL2A1 CASP8 ENDOG PRIMPOL METTL5 RMND1 YRDC GFM2 MRPL27 TFB1M YARS2 GRPEL1 TIMM10 LAP3 PITRM1 ATPAF2 COX5B COX17 NDUFA3 NDUFB10 TMEM70 COX5A PET117 DMAC2L ACLY HMGCL ACSL6 AMACR TAMM41 BCAT2 MCCC1 NUDT2 SUCLG1 COQ7 NFU1 NDUFS8 GTPBP3 GPX4 MTARC2 PRXL2A MTCH1 SLC25A29 MRS2 SMDT1 BCL2L1 CASP9 ERAL1 RECQL4 METTL8 RPUSD3 GRSF1 MRPL28 TRMT61B GRPEL2 TIMM10B LONP1 PMPCA ATPSCKMT COX6A1 COX18 NDUFA5 NDUFB11 COX5B PNKD FMC1 ACO2 HMGCS2 ACSM1 CPT1A TRIAP1 BCKDHA MCCC2 NUDT5 SUCLG2 COQ8A NUBPL NDUFV1 MCCC1 GSR TST SOD1 MTCH2 SLC25A3 MUL1 VDAC1 BCL2L10 CHCHD2 EXD2 RNASEH1 MRM1 RPUSD4 GTPBP10 MRPL3 YBEY HSPD1 TIMM13 MAIP1 PMPCB BCS1L COX6A2 COX19 NDUFA6 NDUFB2 COX6A1 SCO1 MT-ATP6 ACOD1 IDH2 ACSM2A CPT1B BCKDHB PPM1K NUDT9 TK2 COQ8B NDUFV2 MMAA GSTK1 SOD2 ROMO1 SLC25A30 NLRX1 VDAC3 BCL2L11 CYCS EXOG SSBP1 MRM2 SUPV3L1 GUF1 MRPL30 HSPE1 TIMM17A METAP1D SPG7 CEP89 COX6B1 COX20 NDUFA7 NDUFB3 COX6A2 SCO2 MT-ATP8 ACOT11 IDH3A ACSM2B CPT1C BCKDK SLC25A44 PAICS COQ9 NFS1 MMAB GSTZ1 TXN2 SFXN1 SLC25A31 OCIAD2 BCL2L13 DIABLO FARS2 TFAM MRM3 TFB1M HARS2 MRPL32 HTRA2 TIMM17B MIPEP USP30 CMC1 COX6B2 COX7A2L NDUFA8 NDUFB4 COX6B1 SMIM20 TMEM70 ACOT13 IDH3B ACSM3 CPT2 CA5A PPA2 COX10 NFU1 MMADHC HAGH TXNRD1 SFXN2 SLC25A32 PDE2A BCL2L2 ENDOG FASTK TFB2M MRPL12 TRMT10C HEMK1 MRPL33 IDE TIMM21 MUL1 XPNPEP3 CMC2 COX6C DMAC1 NDUFA9 NDUFB5 COX6B2 SURF1 ACOT2 IDH3G ACSM4 CRAT CA5B SLC25A23 COX11 NTHL1 MMUT MAOA TXNRD2 SFXN3 SLC25A33 PINK1 BID GHITM FASTKD1 TOP1MT MRPL47 TRUB2 IARS2 MRPL34 IMMP1L TIMM22 NLN YME1L1 COA1 COX7A1 DMAC2 NDUFAB1 NDUFB6 COX6C TACO1 ACOT7 L2HGDH ACSM5 CROT CHDH SLC25A24 COX15 NUBPL MTFMT MAOB SFXN4 SLC25A34 PPIF BIK HTRA2 FASTKD2 TOP3A MRPS7 KARS1 MRPL35 IMMP2L TIMM23 NRDC COA3 COX7A2 ECSIT NDUFAF1 NDUFB7 COX7A1 TIMM21 ACOT9 LDHAL6B ACSS1 DECR1 COMT SLC25A25 COX17 RSAD1 MTHFD1L MGST1 SFXN5 SLC25A35 PPTC7 BNIP3 IFI27 FASTKD3 TWNK MRPS9 LARS2 MRPL36 LACTB TIMM29 OMA1 COA4 COX7A2L FMC1 NDUFAF2 NDUFB8 COX7A2 TMEM177 ACP6 LDHD ACSS3 ECHS1 CPS1 SLC25A31 COX19 SDHB MTHFD2 MPST SLC25A1 SLC25A36 PRKACA BNIP3L MCL1 FASTKD5 UNG MTERF1 LRPPRC MRPL37 LAP3 TIMM44 PARK7 COA5 COX7B FOXRED1 NDUFAF3 NDUFB9 COX7A2L ACSF2 MCEE AGK ECI1 DBT SLC25A33 CPOX UQCRFS1 MTHFD2L MSRA SLC25A10 SLC25A37 RHOT1 BOK PMAIP1 GADD45GIP1 MTO1 MALSU1 MRPL38 LONP1 TIMM50 PARL COA6 COX7B2 HIGD1A NDUFAF4 NDUFC1 COX7B ACSF3 MDH2 AGPAT4 ECI2 DGLUCY SLC25A36 CPT1A MTHFS MSRB2 SLC25A11 SLC25A38 RHOT2 CASP3 RTL10 GARS1 MTPAP MARS2 MRPL39 MAIP1 TIMM8A PDF COA7 COX7C HIGD2A NDUFAF5 NDUFC2 COX7B2 ACSL1 ME2 AGPAT5 ETFA DHTKD1 SLC25A4 CPT1B MTO1 MSRB3 SLC25A12 SLC25A39 SIRT3 CASP8 SEPTIN4 GATB MTRES1 METAP1D MRPL4 METAP1D TIMM8B PHB COA8 COX8A LYRM2 NDUFAF6 NDUFS1 COX7C ACSL6 ME3 AMACR ETFB DLD SLC25A41 CPT1C PC MTARC1 SLC25A13 SLC25A4 SLC25A12 CASP9 SPHK2 GATC MYG1 METTL17 MRPL40 MIPEP TIMM9 PHB2 COX10 COX8C LYRM7 NDUFAF7 NDUFS2 COX8A ACSM1 MMUT CBR4 ETFDH DLST SLC25A5 CPT2 PCCA MTARC2 SLC25A14 SLC25A40 SLC25A13 CHCHD2 STYXL1 GFM1 NGRN MIEF1 MRPL41 MTX1 TOMM20 PITRM1 COX11 CYC1 NDUFAF1 NDUFAF8 NDUFS3 COX8C ACSM2A MPC1 CHPT1 HADH DMGDH SLC25A6 CYB5B PLPBP NIT1 SLC25A15 SLC25A41 SLC25A23 CHCHD3 GFM2 NOA1 MPV17L2 MRPL42 MTX2 TOMM20L PMPCA COX14 CYCS NDUFAF2 NDUFB1 NDUFS4 HIGD1A ACSM2B MPC1L CPT1A HADHA ECHS1 SUCLA2 CYC1 PNPO NIT2 SLC25A16 SLC25A42 SLC25A24 CHCHD6 GRSF1 NSUN2 MRM2 MRPL43 MUL1 TOMM22 PMPCB COX15 DMAC2L NDUFAF3 NDUFB10 NDUFS5 MT-CO1 ACSM3 MPC2 CPT1B HADHB ETFA SUCLG1 CYCS QDPR OXR1 SLC25A18 SLC25A43 SLC25A25 CYCS GTPBP10 NSUN3 MRM3 MRPL44 NLN TOMM34 PRSS35 COX16 HCCS NDUFAF4 NDUFB11 NDUFS6 MT-CO2 ACSM4 MRPS36 CPT1C HSD17B10 ETFB SUCLG2 CYP11A1 RDH13 PRDX2 SLC25A19 SLC25A44 SLC25A3 DIABLO GTPBP3 NSUN4 MRPL1 MRPL45 NRDC TOMM40 SPG7 COX17 MT-ATP6 NDUFAF5 NDUFB2 NDUFS7 MT-CO3 ACSM5 NEU4 CPT2 MCEE ETFDH TK2 CYP11B1 RDH14 PRDX3 SLC25A20 SLC25A45 SLC25A31 DNAJC11 GUF1 OSGEPL1 MRPL10 MRPL46 OMA1 TOMM40L STOML2 COX18 MT-ATP8 NDUFAF6 NDUFB3 NDUFS8 NDUFA4 ACSS1 OGDH CRAT MMUT GCAT CYP11B2 RFK PRDX4 SLC25A21 SLC25A46 SLC25A4 DNM1L HARS2 PDE12 MRPL11 MRPL47 OXA1L TOMM5 TIMM10 COX19 MT-CO1 NDUFAF7 NDUFB4 NDUFV1 PET100 ACSS3 OGDHL CRLS1 PCCA GCDH CYP24A1 SARDH PRDX5 SLC25A22 SLC25A47 SLC25A5 ENDOG HEMK1 PNPT1 MRPL12 MRPL48 PAM16 TOMM6 TIMM10B COX20 MT-CO2 NDUFAF8 NDUFB5 NDUFV2 PET117 ADHFE1 OXCT1 CROT PCCB GCSH CYP27A1 SFXN1 PRDX6 SLC25A23 SLC25A48 SLC25A6 FIS1 HSD17B10 POLRMT MRPL13 MRPL49 PARK7 TOMM7 TIMM13 COX4I1 MT-CO3 NUBPL NDUFB6 NDUFV3 PNKD AGK OXCT2 CYB5R3 SLC25A20 GLDC CYP27B1 SFXN3 PRXL2A SLC25A24 SLC25A5 SLC8B1 FKBP8 IARS2 PPA2 MRPL14 MRPL50 PARL TOMM70 TIMM8A COX4I2 MT-CYB PET100 NDUFB7 SCO1 AGMAT PC CYP11A1 GLS DNA2 SHMT2 SELENOO SLC25A25 SLC25A51 SMDT1 FUNDC1 KARS1 PRORP MRPL15 MRPL51 PDF UQCRC1 TIMM8B COX5A MT-ND1 PET117 NDUFB8 SCO2 AGPAT4 PCCA CYP11B1 GLS2 ETFDH SLC25A19 SOD1 SLC25A26 SLC25A52 SPHKAP FUNDC2 LACTB2 PTCD1 MRPL16 MRPL52 PHB UQCRC2 TIMM9 COX5B MT-ND2 PNKD NDUFB9 SMIM20 AGPAT5 PCCB CYP11B2 GLUD1 FABP1 SLC25A32 SOD2 SLC25A27 SLC25A53 VDAC1 GHITM LARS2 PTCD2 MRPL17 MRPL53 PHB2 XPNPEP3 TRAP1 COX6A1 MT-ND3 RAB5IF NDUFC1 SURF1 AGXT PCK2 CYP27A1 GLUD2 FAM210B SLC25A38 TST SLC25A28 SLC25A6 VDAC3 HTRA2 LIG3 PUS1 MRPL18 MRPL54 PITRM1 USP30 COX6A2 MT-ND4 SCO1 NDUFC2 TACO1 AGXT2 PDHA1 DBI GLYAT FDX1 TXN2 TXN2 SLC25A29 UCP1 IFI27 LRPPRC QTRT1 MRPL19 MRPL55 PMPCA XPNPEP3 COX6B1 MT-ND4L SCO2 NDUFS1 TIMM21 AIFM2 PDHA2 DECR1 GOT2 FDX2 TXNRD1 SLC25A3 UCP2 IMMT MALSU1 RCC1L MRPL2 MRPL57 PMPCB YME1L1 COX6B2 MT-ND5 SDHAF1 NDUFS2 TMEM177 AIFM3 PDHB DHRS1 GPT2 FDXR TXNRD2 SLC25A30 UCP3 MARCHF5 MARS2 REXO2 MRPL20 MRPL58 PRSS35 COX6C MT-ND6 SDHAF2 NDUFS3 AK2 PDHX ECH1 GRHPR FECH SLC25A31 MCL1 METAP1D RMND1 MRPL21 MRPL9 ROMO1 COX7A1 NDUFA1 SDHAF3 NDUFS4 AK3 PDK1 ECHDC1 HADH FTH1 SLC25A32 MFF METTL15 RNASEH1 MRPL22 MRPS10 SAMM50 COX7A2 NDUFA10 SDHAF4 NDUFS5 AK4 PDK2 ECHS1 HADHA FTMT SLC25A33 MFN1 METTL17 RPUSD3 MRPL23 MRPS11 SPG7 COX7A2L NDUFA11 SMIM20 NDUFS6 AKR1B10 PDK3 ECI1 HADHB FXN SLC25A34 MFN2 METTL4 RPUSD4 MRPL24 MRPS12 STOML2 COX7B NDUFA12 SURF1 NDUFS7 AKR7A2 PDK4 ECI2 HIBADH GLRX2 SLC25A35 MGARP METTL5 SLIRP MRPL27 MRPS14 TIMM10 COX7B2 NDUFA13 TACO1 NDUFS8 ALAS1 PDP1 EHHADH HIBCH GLRX5 SLC25A36 MICOS10 METTL8 SUPV3L1 MRPL28 MRPS15 TIMM10B COX7C NDUFA2 TIMM21 NDUFV1 ALAS2 PDP2 EPHX2 HMGCL GRPEL1 SLC25A37 MICOS13 MGME1 TBRG4 MRPL3 MRPS16 TIMM13 COX8A NDUFA3 TIMMDC1 NDUFV2 ALDH18A1 PDPR ETFA HOGA1 GRPEL2 SLC25A38 MIEF1 MIEF1 TEFM MRPL30 MRPS17 TIMM17A COX8C NDUFA4 TMEM126A NDUFV3 ALDH1B1 RPIA ETFB HSD17B10 HCCS SLC25A39 MIEF2 MPV17L2 TFAM MRPL32 MRPS18A TIMM17B CYC1 NDUFA5 TMEM126B NUBPL ALDH1L1 SDHA ETFDH IVD HSCB SLC25A4 MIGA1 MRM1 TFB1M MRPL33 MRPS18B TIMM21 CYCS NDUFA6 TMEM177 TIMMDC1 ALDH1L2 SDHB FABP1 KMO HSPA9 SLC25A40 MIGA2 MRM2 TFB2M MRPL34 MRPS18C TIMM22 DMAC1 NDUFA7 TMEM186 TMEM126A ALDH2 SDHC FASN KYAT3 IBA57 SLC25A41 MTCH2 MRM3 THG1L MRPL35 MRPS2 TIMM23 DMAC2 NDUFA8 TMEM70 TMEM126B ALDH3A2 SDHD FDPS LDHB ISCA1 SLC25A42 MTFP1 MRPL1 TOP1MT MRPL36 MRPS21 TIMM29 DMAC2L NDUFA9 TTC19 TMEM186 ALDH4A1 SFXN5 FDX1 MAOA ISCA2 SLC25A43 MTFR1 MRPL10 TRIT1 MRPL37 MRPS22 TIMM44 ECSIT NDUFAB1 UQCC1 TMEM70 ALDH5A1 SLC25A1 FDXR MAOB ISCU SLC25A44 MTFR2 MRPL11 TRMT1 MRPL38 MRPS23 TIMM50 FMC1 NDUFB1 UQCC2 ALDH6A1 SLC25A10 GCSH MCCC1 KMO SLC25A45 MTX1 MRPL12 TRMT10C MRPL39 MRPS24 TIMM8A FOXRED1 NDUFB10 UQCC3 ALDH7A1 SLC25A11 GPAM MCCC2 KYAT3 SLC25A46 MTX2 MRPL13 TRMT2B MRPL4 MRPS25 TIMM8B HCCS NDUFB11 ALDH9A1 SLC25A12 GPAT2 NAGS LIAS SLC25A47 MTX3 MRPL14 TRMT5 MRPL40 MRPS26 TIMM9 HIGD1A NDUFB2 AMACR SLC25A13 HADH NAT8L LYRM4 SLC25A48 MUL1 MRPL15 TRMT61B MRPL41 MRPS27 TOMM20 HIGD2A NDUFB3 AMT SUCLA2 HADHA OAT MOCS1 SLC25A5 MYO19 MRPL16 TRMU MRPL42 MRPS28 TOMM20L LYRM2 NDUFB4 ANTKMT SUCLG1 HADHB OTC MT-CO1 SLC25A51 NBR1 MRPL17 TRNT1 MRPL43 MRPS30 TOMM22 LYRM7 NDUFB5 ARG2 SUCLG2 HAO2 PPM1K MT-CYB SLC25A52 NIPSNAP1 MRPL18 TRUB2 MRPL44 MRPS31 TOMM34 MT-ATP6 NDUFB6 AUH HINT2 PRODH MTARC1 SLC25A53 NIPSNAP2 MRPL19 YBEY MRPL45 MRPS33 TOMM40 MT-ATP8 NDUFB7 BCAT2 HSD17B10 PRODH2 MTARC2 SLC25A6 OMA1 MRPL2 YRDC MRPL46 MRPS34 TOMM40L MT-CO1 NDUFB8 BCKDHA HSD17B4 PYCR1 NADK2 SLC30A9 OPA1 MRPL20 MRPL47 MRPS35 TOMM5 MT-CO2 NDUFB9 BCKDHB HSD17B8 PYCR2 NAXD SLC8B1 PARK7 MRPL21 MRPL48 MRPS36 TOMM6 MT-CO3 NDUFC1 BCKDK HTD2 SARDH NAXE SMDT1 PARL MRPL22 MRPL49 MRPS5 TOMM7 MT-CYB NDUFC2 BCO2 IDI1 SDSL NDUFAB1 STARD7 PGAM5 MRPL23 MRPL50 MRPS6 TOMM70 MT-ND1 NDUFS1 BDH1 LACTB SFXN1 NDUFS1 UCP1 PIGBOS1 MRPL24 MRPL51 MRPS7 TRAP1 MT-ND2 NDUFS2 BOLA1 LIAS SFXN3 NDUFS2 UCP2 PINK1 MRPL27 MRPL52 MRPS9 UQCRC1 MT-ND3 NDUFS3 BOLA3 LIPT1 SHMT2 NDUFS7 UCP3 PLD6 MRPL28 MRPL53 PTCD3 UQCRC2 MT-ND4 NDUFS4 BPHL LIPT2 SLC25A12 NDUFS8 VDAC1 PMAIP1 MRPL3 MRPL54 USP30 MT-ND4L NDUFS5 CA5A LYPLA1 SLC25A13 NDUFV1 VDAC2 PRKN MRPL30 MRPL55 XPNPEP3 MT-ND5 NDUFS6 CA5B LYPLAL1 SLC25A15 NDUFV2 VDAC3 RAB24 MRPL32 MRPL57 YME1L1 MT-ND6 NDUFS7 CAT MCAT SLC25A21 NFS1 RHOT1 MRPL33 MRPL58 NDUFA1 NDUFS8 CBR3 MCEE SLC25A29 NFU1 RHOT2 MRPL34 MRPL9 NDUFA10 NDUFV1 CBR4 MECR SLC25A38 NMNAT3 RMDN3 MRPL35 MRPS10 NDUFA11 NDUFV2 CHCHD7 MGST3 SLC25A44 NNT RTL10 MRPL36 MRPS11 NDUFA12 NDUFV3 CHDH MLYCD SUGCT NOCT SAMM50 MRPL37 MRPS12 NDUFA13 SDHA CHPT1 MMUT NTHL1 SEPTIN4 MRPL38 MRPS14 NDUFA2 SDHB CISD1 NDUFAB1 NUBPL SLC25A46 MRPL39 MRPS15 NDUFA3 SDHC CISD3 OSBPL1A NUDT13 SNAP29 MRPL4 MRPS16 NDUFA4 SDHD CKMT1A OXSM NUDT19 SPHK2 MRPL40 MRPS17 NDUFA5 UQCR10 CKMT1B PCCA NUDT8 SPIRE1 MRPL41 MRPS18A NDUFA6 UQCR11 CKMT2 PCCB PANK2 STX17 MRPL42 MRPS18B NDUFA7 UQCRB CLYBL PGS1 PCBD2 STYXL1 MRPL43 MRPS18C NDUFA8 UQCRC1 CMPK2 PHYH PDSS1 SYNJ2BP MRPL44 MRPS2 NDUFA9 UQCRC2 COASY PISD PDSS2 TMEM11 MRPL45 MRPS21 NDUFAB1 UQCRFS1 COMT PLD6 PPOX TOMM20 MRPL46 MRPS22 NDUFAF1 UQCRH COQ10A PLSCR3 QDPR TOMM7 MRPL47 MRPS23 NDUFAF2 UQCRQ COQ10B PNPLA8 RSAD1 USP30 MRPL48 MRPS24 NDUFAF3 COQ2 PRDX6 SCO1 VDAC1 MRPL49 MRPS25 NDUFAF4 COQ3 PRELID1 SCO2 VPS13D MRPL50 MRPS26 NDUFAF5 COQ4 PRELID3A SDHB MRPL51 MRPS27 NDUFAF6 COQ5 PRELID3B SDHC MRPL52 MRPS28 NDUFAF7 COQ6 PTGES2 SDHD MRPL53 MRPS30 NDUFAF8 COQ7 PTPMT1 SIRT3 MRPL54 MRPS31 NDUFB1 COQ8A SCP2 SIRT4 MRPL55 MRPS33 NDUFB10 COQ8B SERAC1 SIRT5 MRPL57 MRPS34 NDUFB11 COQ9 SLC25A1 SLC25A20 MRPL58 MRPS35 NDUFB2 COX10 SLC25A20 SLC25A28 MRPL9 MRPS36 NDUFB3 COX11 SPHK2 SLC25A3 MRPS10 MRPS5 NDUFB4 COX15 SPTLC2 SLC25A37 MRPS11 MRPS6 NDUFB5 COX17 STAR SLC25A38 MRPS12 MRPS7 NDUFB6 COX19 STARD7 SLC25A42 MRPS14 MRPS9 NDUFB7 CPOX TAMM41 SLC25A51 MRPS15 MRRF NDUFB8 CPS1 TAZ SLC25A52 MRPS16 MTERF3 NDUFB9 CPT1A THEM4 SPR MRPS17 MTERF4 NDUFC1 CPT1B THEM5 SUOX MRPS18A MTFMT NDUFC2 CPT1C TRIAP1 TMLHE MRPS18B MTG1 NDUFS1 CPT2 TSPO UQCRFS1 MRPS18C MTG2 NDUFS2 CRAT ZADH2 MRPS2 MTIF2 NDUFS3 CRLS1 MRPS21 MTIF3 NDUFS4 CROT MRPS22 MTRES1 NDUFS5 CS MRPS23 MTRF1 NDUFS6 CYB5B MRPS24 MTRF1L NDUFS7 CYB5R3 MRPS25 NARS2 NDUFS8 CYC1 MRPS26 NGRN NDUFV1 CYCS MRPS27 NOA1 NDUFV2 CYP11A1 MRPS28 NSUN4 NDUFV3 CYP11B1 MRPS30 OXA1L NUBPL CYP11B2 MRPS31 PARS2 PET100 CYP24A1 MRPS33 PDF PET117 CYP27A1 MRPS34 PPA2 PNKD CYP27B1 MRPS35 PTCD3 RAB5IF D2HGDH MRPS36 PUSL1 SCO1 DBI MRPS5 QRSL1 SCO2 DBT MRPS6 RARS2 SDHA DCXR MRPS7 RBFA SDHAF1 DECR1 MRPS9 RMND1 SDHAF2 DGLUCY MRRF SARS2 SDHAF3 DGUOK MTERF1 SLIRP SDHAF4 DHODH MTERF2 TACO1 SDHB DHRS1 MTERF3 TARS2 SDHC DHRS2 MTERF4 TFB1M SDHD DHRS4 MTFMT TIMM21 SMIM20 DHTKD1 MTG1 TRMT61B SURF1 DLAT MTG2 TSFM TACO1 DLD MTIF2 TUFM TIMM21 DLST MTIF3 VARS2 TIMMDC1 DMGDH MTO1 WARS2 TMEM126A DNA2 MTPAP YARS2 TMEM126B DTYMK MTRES1 YBEY TMEM177 DUT MTRF1 TMEM186 ECH1 MTRF1L TMEM70 ECHDC1 MUTYH TTC19 ECHS1 MYG1 UQCC1 ECI1 NARS2 UQCC2 ECI2 NGRN UQCC3 EHHADH NOA1 UQCR10 EPHX2 NSUN2 UQCR11 ETFA NSUN3 UQCRB ETFB NSUN4 UQCRC1 ETFBKMT OGG1 UQCRC2 ETFDH OSGEPL1 UQCRFS1 ETFRF1 OXA1L UQCRH ETHE1 PARS2 UQCRQ FABP1 PDE12 FAHD1 PDF FAM210B PIF1 FASN PNPT1 FDPS POLB FDX1 POLDIP2 FDX2 POLG FDXR POLG2 FECH POLQ FH POLRMT FHIT PPA2 FLAD1 PRIMPOL FPGS PRORP FTH1 PTCD1 FTMT PTCD2 FXN PTCD3 GATM PUS1 GCAT PUSL1 GCDH QRSL1 GCSH QTRT1 GLDC RARS2 GLRX2 RBFA GLRX5 RCC1L GLS RECQL4 GLS2 REXO2 GLUD1 RMND1 GLUD2 RNASEH1 GLYAT RPUSD3 GLYCTK RPUSD4 GOT2 SARS2 GPAM SLIRP GPAT2 SSBP1 GPD2 SUPV3L1 GPT2 TACO1 GPX1 TARS2 GPX4 TBRG4 GRHPR TEFM GRPEL1 TFAM GRPEL2 TFB1M GSR TFB2M GSTK1 THG1L GSTZ1 TIMM21 GTPBP3 TOP1MT GUK1 TOP3A HADH TRIT1 HADHA TRMT1 HADHB TRMT10C HAGH TRMT2B HAO2 TRMT5 HCCS TRMT61B HIBADH TRMU HIBCH TRNT1 HINT1 TRUB2 HINT2 TSFM HMGCL TUFM HMGCS2 TWNK HOGA1 UNG HSCB VARS2 HSD17B10 WARS2 HSD17B4 YARS2 HSD17B8 YBEY HSPA9 YRDC HTD2 IBA57 IDH2 IDH3A IDH3B IDH3G IDI1 ISCA1 ISCA2 ISCU IVD KMO KYAT3 L2HGDH LACTB LDHAL6B LDHB LDHD LIAS LIPT1 LIPT2 LYPLA1 LYPLAL1 LYRM4 MAOA MAOB MCAT MCCC1 MCCC2 MCEE MDH2 ME2 ME3 MECR MGST1 MGST3 MLYCD MMAA MMAB MMADHC MMUT MOCS1 MPC1 MPC1L MPC2 MPST MRPS36 MSRA MSRB2 MSRB3 MT-CO1 MT-CYB MTARC1 MTARC2 MTFMT MTHFD1L MTHFD2 MTHFD2L MTHFS MTO1 NADK2 NAGS NAT8L NAXD NAXE NDUFAB1 NDUFS1 NDUFS2 NDUFS7 NDUFS8 NDUFV1 NDUFV2 NEU4 NFS1 NFU1 NIT1 NIT2 NME3 NME4 NME6 NMNAT3 NNT NOCT NT5DC2 NT5M NTHL1 NUBPL NUDT13 NUDT19 NUDT2 NUDT5 NUDT8 NUDT9 OAT OGDH OGDHL OSBPL1A OTC OXCT1 OXCT2 OXR1 OXSM PAICS PANK2 PC PCBD2 PCCA PCCB PCK2 PDHA1 PDHA2 PDHB PDHX PDK1 PDK2 PDK3 PDK4 PDP1 PDP2 PDPR PDSS1 PDSS2 PGS1 PHYH PISD PLD6 PLPBP PLSCR3 PNPLA8 PNPO PPA2 PPM1K PPOX PRDX2 PRDX3 PRDX4 PRDX5 PRDX6 PRELID1 PRELID3A PRELID3B PRODH PRODH2 PRXL2A PTGES2 PTPMT1 PYCR1 PYCR2 QDPR RDH13 RDH14 RFK RPIA RSAD1 SARDH SCO1 SCO2 SCP2 SDHA SDHB SDHC SDHD SDSL SELENOO SERAC1 SFXN1 SFXN3 SFXN5 SHMT2 SIRT3 SIRT4 SIRT5 SLC25A1 SLC25A10 SLC25A11 SLC25A12 SLC25A13 SLC25A14 SLC25A15 SLC25A19 SLC25A20 SLC25A21 SLC25A23 SLC25A24 SLC25A25 SLC25A28 SLC25A29 SLC25A3 SLC25A30 SLC25A31 SLC25A32 SLC25A33 SLC25A36 SLC25A37 SLC25A38 SLC25A4 SLC25A41 SLC25A42 SLC25A44 SLC25A5 SLC25A51 SLC25A52 SLC25A6 SOD1 SOD2 SPHK2 SPR SPTLC2 SQOR STAR STARD7 SUCLA2 SUCLG1 SUCLG2 SUGCT SUOX TAMM41 TAZ THEM4 THEM5 TK2 TMLHE TRIAP1 TSPO TST TSTD1 TXN2 TXNRD1 TXNRD2 UQCRFS1 ZADH2